include asthenia, fever, weight loss, splenomegaly, hepatomegaly, generalized lymphadenopathy, peripheral edema, pleural effusion, impaired renal function, and sometimes polyneuropathy. It is also associated with an acquired immunodeficiency syndrome, Kaposi\'s sarcoma, POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M protein, and skin change), and amyloidosis \[[@B11]--[@B13]\]. Sometimes CD is detected incidentally as a slow-growing mass. The unicentric hyaline-vascular type of CD rarely shows systemic symptoms (\<10%) \[[@B3], [@B14]\]. The most commonly described (77--91%) symptoms in the literature is a localized \[[@B3], [@B14]\] and an asymptomatic mass \[[@B3], [@B15]\]. A recently published series of eight cases of peripancreatic unicentric CD showed that most of the patients were asymptomatic and few cases complained of vague abdominal pain. In that series, the most common histological variety was the hyaline vascular form \[[@B16]\].

Ultrasound and CT or MRI imaging modalities cannot diagnose CD because of the lack of tumor-specific signs but give information about the exact tumor location \[[@B7]\]. Other nonspecific diagnostic abnormalities include anemia, hypoalbuminemia, polyclonal gammopathy, elevated erythrocyte sedimentation rate or C-reactive protein concentration, and proteinuria \[[@B17]\], which is not found in the localized form. Gallium scintigraphy is considered sensitive for diagnosis and detection of the hyaline-vascular type of CD, but in the plasma cell variant, it is debated \[[@B18]\]. Only surgical resection and conventional histological evaluation can give an accurate characterization of this tumor.

Treatment of the unicentric CD (UCD) is the resection, which gives excellent long-term results \[[@B6]\]. Radiotherapy is also considered a treatment option for patients with poor surgical approach or had surgery with incomplete resection \[[@B7]\]. In patients with the multicentric CD, surgical treatment is not beneficial and steroid treatment is the mainstay, with or